Double aortic arch is a type of vascular ring heart defect. In a normal heart, the blood flows in from the body to the right atrium, goes into the right ventricle, and then goes to the lungs to pick up fresh oxygen. The blood returns to the left atrium, goes into the left ventricle, and goes out to the rest of the body through a large artery called the aorta.
With a double aortic arch, the aorta branches into right and left tubes, instead of just being 1 large tube. The 2 tubes can circle around and compress the airways and/or esophagus.
Double aortic arch is a congenital defect. This means that the baby is born with the condition. It is not known exactly why the heart develops abnormally in some babies.
Symptoms may include:
While this condition may be detected in infancy, it is often found later.
You will be asked about your child’s symptoms and medical history. A physical exam will be done.
Your child's bodily structures may need to be viewed. This can be done with:
Your child's heart activity may need to be measured. This can be done with an electrocardiogram.
Talk with your doctor about the best treatment plan for your child. Treatment options include:
If your child is having symptoms like difficulty breathing, surgery will be done. The goal of surgery is to tie off and close 1 of the extra branches. After this is done, symptoms may improve right away or gradually over time.
American Heart Association
Healthy Children—American Academy of Pediatrics
Canadian Cardiovascular Society
Heart and Stroke Foundation of Canada
Double aortic arch. Johns Hopkins University, Cove Point Foundation website. Available at: http://www.pted.org/?id=doubleaortic1. Updated May 16, 2011. Accessed June 6, 2016.
Vascular ring. Children’s Hospital Boston website. Available at: http://www.childrenshospital.org/az/Site1942/mainpageS1942P0.html. Accessed June 6, 2016.
Last reviewed June 2016 by Karri Kassir, MD
Please be aware that this information is provided to supplement the care provided by your physician. It is neither intended nor implied to be a substitute for professional medical advice. CALL YOUR HEALTHCARE PROVIDER IMMEDIATELY IF YOU THINK YOU MAY HAVE A MEDICAL EMERGENCY. Always seek the advice of your physician or other qualified health provider prior to starting any new treatment or with any questions you may have regarding a medical condition.