A vascular ring is a defect of the aorta and nearby large vessels. The aorta is the large artery that carries blood from the heart to the body. When the aorta and nearby large vessels form in abnormal positions, the trachea and esophagus can become constricted by the “ring” formed by these abnormal vessels. Examples of this type of defect include:
While vascular ring may be detected in infancy, it is often discovered later in life.
Vascular ring is a congenital defect. This means that the baby is born with the condition. During fetal growth in the womb, the large vessels near the heart do not develop normally. It is not known exactly why some children’s vessels develop in this way.
Symptoms vary and can range from mild to severe. They may include:
These symptoms may be caused by other conditions. If your child has any of these, tell the doctor right away.
Your doctor will ask about your child’s symptoms and medical history. A physical exam will be done. Tests may include:
Talk with your doctor about the best treatment plan for your child. Treatment options include:
The goal of surgery is to divide the vascular ring and relieve compression on the trachea and esophagus. This surgery may even be done if your child has minor symptoms.
Before surgery, the doctor will treat your child’s symptoms. For example, the doctor will make sure that your child gets proper nutrition if he has swallowing problems. If your child has a bacterial respiratory infection, he will be treated with antibiotics.
American Family Physician
American Heart Association
Canadian Cardiovascular Society
Heart and Stroke Foundation of Canada
Children’s Hospital Boston. Vascular ring. Children’s Hospital Boston website. Available at: http://www.childrenshospital.org/az/Site1942/mainpageS1942P0.html. Accessed July 23, 2010.
Cincinnati Children’s Hospital. Vascular rings. Cincinnati Children’s Hospital website. Available at: http://www.cincinnatichildrens.org/health/heart-encyclopedia/anomalies/rings.htm. Accessed July 23, 2010.
Johns Hopkins University, Cove Point Foundation. Vascular ring. Johns Hopkins University, Cove Point Foundation website. Available at: http://www.pted.org/?id=vascularring2. Accessed July 9, 2010.
Last reviewed June 2013 by Michael Woods, MD
Please be aware that this information is provided to supplement the care provided by your physician. It is neither intended nor implied to be a substitute for professional medical advice. CALL YOUR HEALTHCARE PROVIDER IMMEDIATELY IF YOU THINK YOU MAY HAVE A MEDICAL EMERGENCY. Always seek the advice of your physician or other qualified health provider prior to starting any new treatment or with any questions you may have regarding a medical condition.