An atrioventricular (AV) canal defect is a rare heart defect. There is a large hole in the center of the heart that connects all four chambers.
The heart is made up of two upper chambers and two lower chambers. Usually blood flows from the upper to lower chamber on the right side of the heart to the lungs. The blood picks up oxygen in the lungs and passes back into the upper chamber of the left side of the heart. It then passes to the lower chamber of the heart and out to the body.
The AV canal defect causes blood in the different chambers to mix. This means that some of the blood that is sent out to the body has not passed the lungs to pick up oxygen. The body does not get enough oxygen.
AV canal defect is a congenital defect. This means that the baby is born with it. It is not known exactly why some babies’ hearts develop abnormally.
Factors that increase the risk of congenital heart defects include:
Symptoms may include:
This condition can lead to heart failure. If your child has any of these symptoms, get medical care right away.
The doctor will ask about your child’s symptoms and medical history. A physical exam will be done. Imaging tests may be done to view your heart's structures:
Talk with the doctor about the best treatment plan for your child. Treatment options include:
Surgery is usually recommended to correct the defect. The goal of surgery is to close the hole with a patch.
After surgery, your child will need to have regular visits with a heart doctor. The doctor may recommend that your child:
American Family Physician
American Heart Association
Canadian Cardiovascular Society
Heart and Stroke Foundation of Canada
Atrioventricular canal defect. American Heart Association website. Available at: http://www.heart.org/HEARTORG/Conditions/CongenitalHeartDefects/AboutCongenitalHeartDefects/Complete-Atrioventricular-Canal-defect-CAVC_UCM_307023_Article.jsp. Accessed June 21, 2013.
Atrioventricular canal defect. Boston Children's Hospital website. Available at: http://www.childrenshospital.org/az/Site521/mainpageS521P0.html. Accessed June 21, 2013.
Ventricular septal defect (VSD). EBSCO DynaMed website. Available at: http://www.ebscohost.com/dynamed/what.php. Updated June 14, 2012. Accessed June 21, 2013.
Last reviewed June 2013 by Michael Woods, MD
Please be aware that this information is provided to supplement the care provided by your physician. It is neither intended nor implied to be a substitute for professional medical advice. CALL YOUR HEALTHCARE PROVIDER IMMEDIATELY IF YOU THINK YOU MAY HAVE A MEDICAL EMERGENCY. Always seek the advice of your physician or other qualified health provider prior to starting any new treatment or with any questions you may have regarding a medical condition.